Diagnosis and Management of Hydroa Vacciniforme


  • Reisa Reshinta Department of Dermatology and Venereology, Faculty of Medicine, University of Indonesia - RSUPN dr. Cipto Mangunkusumo, Jakarta, Indonesia
  • Githa Rahmayunita Department of Dermatology and Venereology, Faculty of Medicine, University of Indonesia - RSUPN dr. Cipto Mangunkusumo, Jakarta, Indonesia
  • Rahadi Rihatmadja Department of Dermatology and Venereology, Faculty of Medicine, University of Indonesia - RSUPN dr. Cipto Mangunkusumo, Jakarta, Indonesia
  • Rinadewi Astriningrum Department of Dermatology and Venereology, Faculty of Medicine, University of Indonesia - RSUPN dr. Cipto Mangunkusumo, Jakarta, Indonesia




hydroa vacciniforme, diagnosis, photodermatoses, management


Hydroa vacciniforme (HV) is a rare photodermatoses with the most frequent onset in childhood. The exact pathogenesis of HV is still not known. This disease is a spectrum with almost similar clinical symptoms, but with a very different prognosis. Classic HV has the best prognosis, but affects the quality of life due to scar formation, while hydroa vacciniforme-like lymphoma (HVLL) is the variant with the worst prognosis. HV needs to be considered as a differential diagnosis, especially in childhood-onset photodermatoses. Classical HV must be distinguishes from hydroa vacciniforme-like lymphoproliferative disorders (HVLPD) because it is related to prognosis. There is still no consensus or guidelines on diagnosis and management for HV. 


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How to Cite

Reshinta, R., Rahmayunita, G., Rihatmadja, R., & Astriningrum, R. (2024). Diagnosis and Management of Hydroa Vacciniforme. Cermin Dunia Kedokteran, 51(5), 255–260. https://doi.org/10.55175/cdk.v51i5.902