Glaukoma Kongenital Primer
Tinjauan Pustaka
DOI:
https://doi.org/10.55175/cdk.v53i03.1576Kata Kunci:
Children, glaucoma, primary congenital glaucoma, increased intraocular pressureAbstrak
Glaukoma kongenital primer adalah glaukoma yang disebabkan oleh gangguan perkembangan sudut bilik mata anterior, khususnya trabecular meshwork yang menghambat aliran keluarnya aqueous humor dan menyebabkan peningkatan tekanan intraokular. Kondisi ini merupakan salah satu penyebab utama kebutaan pada anak-anak dan memiliki dampak jangka panjang terhadap perkembangan visual serta kualitas hidup pasien. Lebih dari 75% glaukoma kongenital primer didiagnosis dalam 12 bulan pertama setelah lahir, bahkan pada kasus yang berat, glaukoma sudah terdeteksi saat bayi lahir. Peningkatan tekanan intraokular yang tidak segera ditangani dapat menimbulkan kerusakan permanen pada saraf optik, pembesaran bola mata (buphthalmos), edema dan kekeruhan kornea, serta defek lapang pandang progresif. Diagnosis umumnya ditegakkan berdasarkan gambaran klinis khas berupa epifora, fotofobia, dan blefarospasme, disertai pemeriksaan oftalmologis menyeluruh. Penatalaksanaan utama bersifat bedah dengan tujuan menurunkan tekanan intraokular dan mencegah komplikasi lebih lanjut. Deteksi dini dan intervensi yang tepat sangat penting untuk mempertahankan fungsi visual dan mencegah gangguan penglihatan permanen pada anak.
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Referensi
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