Laporan Kasus Kekeruhan Kornea Kongenital: Tantangan Operasi Keratoplasti pada Anak-Anak
Laporan Kasus
DOI:
https://doi.org/10.55175/cdk.v52i11.1712Kata Kunci:
Disgenesis segmen anterior, laporan kasus, opasitas kornea kongenital, graft kornea, keratoplastiAbstrak
Pendahuluan: Opasitas kornea kongenital atau congenital corneal opacity (CCO) adalah sekelompok disgenesis segmen anterior yang ditandai dengan hilangnya transparansi kornea sejak lahir atau dalam 4 minggu pertama kehidupan. CCO merupakan salah satu entitas penyakit yang paling menonjol dalam disgenesis segmen anterior. CCO disebabkan oleh gangguan dalam perkembangan mesodermal, terutama memengaruhi segmen anterior mata. Kasus: Neonatus laki-laki berusia 2 minggu dengan CCO bilateral. Satu minggu pasca-operasi keratoplasti, orang tua pasien melaporkan tidak ada keluhan, namun pemberian obat tetes mata sulit karena pasien tidak kooperatif. Pemeriksaan fisik menunjukkan graft kornea yang lebih jernih. Satu bulan kemudian, ditemukan graft keruh dan beberapa jahitan lepas, yang mengindikasikan penolakan graft. Keluarga pasien telah diedukasi tentang pentingnya penggunaan obat secara konsisten untuk operasi graft di masa mendatang. Diskusi: Pilihan bedah untuk CCO adalah cangkok kornea atau keratoplasti. Keratoplasti adalah transplantasi kornea di mana cangkok donor yang bening menggantikan kornea sentral yang buram. Simpulan: Pemeriksaan menyeluruh sangat penting dalam diagnosis CCO. Keratoplasti dapat mengembalikan kejernihan kornea dan penglihatan, namun pada kasus pediatrik diperlukan edukasi pasien yang lebih cermat dan pemantauan lanjutan yang
komprehensif.
Unduhan
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