Tata Laksana Kraniofaringioma Anak

Penulis

  • Srisabrina Christia Dokter Umum. RS Pelita Kasih, Sangatta, Kabupaten Kutai Timur, Kalimantan Timur, Indonesia
  • Nurul Hidaya Dokter Umum, PKM Belawae, Kabupaten Sidenreng Rappang, Sulawesi Selatan, Indonesia

DOI:

https://doi.org/10.55175/cdk.v51i3.904

Kata Kunci:

Kelenjar hipofisis, kraniofaringioma, neuroepitelial

Abstrak

Kraniofaringioma adalah tumor jinak neuroepitelial di sekitar kelenjar hipofisis. Dua tipe kraniofaringioma berdasarkan morfologinya, yaitu tipe adamantinomatous (ACP) yang lebih sering dijumpai dan tipe papiler (PCP). Gejala yang sering dijumpai saat diagnosis adalah defisiensi hipotalamus/hipofisis, gangguan penglihatan, dan peningkatan tekanan intrakranial. Tujuan pembedahan, baik reseksi total maupun subtotal, adalah dekompresi jaras optik dan ventrikel. Radioterapi setelah reseksi subtotal memberikan hasil yang lebih baik dibandingkan hanya reseksi subtotal. Radiasi dapat dilakukan pada anak usia >3 tahun, namun pada praktiknya lebih sering pada anak usia >5 tahun. Tata laksana kraniofaringioma membutuhkan tim multidisiplin.

Unduhan

Data unduhan belum tersedia.

Referensi

Muller HL, Otte A. Childhood-onset craniopharyngioma. J Clin Endocrinol Metabolism. 2021;106(10):3820-36.

Serbis A, Tsinopoulou VR, Papadopoulou A, Kolanis S, Sakellari EI, Margaritis K, et al. Predictive factors for pediatric craniopharyngioma recurrence: An extensive narrative review. Diagnostics 2023;13(9):1588.

Muller HL, Merchant TE, Warmuth-Metz M, Martinez-Barbera JP, Puget S. Craniopharyngioma. Nature Rev. 2019;5:75.

Torres MO, Shafiq I, Mesfin FB. Pediatric craniopharyngioma. National Library of Medicine [Internet]. 2022. Available from: https://www.ncbi.nlm.nih.gov/books/NBK519027/.

Drapeau A, Walz PC, Eide JG, Rugino AJ, Shaikhouni A, Mohyeldin A, et al. Pediatric craniopharyngioma. Child’s Nervous System 2019;35:2133-45.

Diaz MJ, Kwak SH, Root KT, Fadil A, Nguyen A, Ladehoff L, et al. Current approaches to craniopharyngioma management. Front. Biosci. 2022;27 (12):328.

Lithgow K, Hamblin R, Karavitaki N. Craniopharyngiomas. National Library of Medicine [Internet]. 2022. Available from: https://www.ncbi.nlm.nih.gov/books/NBK538819/.

Greenberg MS. Handbook of neurosurgery. 9th Ed. New York: Thieme; 2020.

Krisht KM, Gottfried ON, Couldwell WT. Craniopharyngioma. In: Bernstein M, Berger MS, editors. Neuro-oncology the essential. 3rd Ed. New York: Thieme; 2015 .p. 418-28.

Lee IH, Zan E, Bell WR, Burger PC, Sung H, Yousem DM. Craniopharyngiomas: Radiological differentiation of two types. J Korean Neurosurg. 2016;59(5):466-70.

Huang CC, Lin KL, Wu CT, Jung SM, Wang CJ, Chen YC, et al. Clinical and endocrinological manifestations of childhood-onset craniopharyngioma before surgical removal: A report from one medical center in Taiwan. Pediatr Neonatol. 2021;62(2):181-6

Muller HL. The diagnosis and treatment of craniopharyngiomas. Neuroendocrinol. 2020;110:753–66.

Frühwald MC, Rutkowski S. Tumors of the central nervous system in children and adolescents. Dtsch Arztebl Int. 2011;108(22):390-7.

Zhou Z, Zhang S, Hu F. Endocrine disorder in patients with craniopharyngioma. Front Neurol. 2021;12:737743

Hendricks BK. The neurosurgical atlas [Internet]. 2022. Available from: https://www.neurosurgicalatlas.com/volumes/cranial-base-surgery/other-skull-base-tumors/craniopharyngioma-transcranial-approach.

Ravindra VM, Okcu MF, Ruggieri L, Frank TS, Paulino AC, McGovern SL , et al. Comparison of multimodal surgical and radiation treatment methods for pediatric craniopharyngioma long-term analysis of progression-free survival and morbidity. J Neurosurg Pediatr. 2021;28(2):152-9

Alkhalidi H, Hawkins CE. Histopathological features of common pediatric brain tumors. In: Mehta MP, editor. Principles and practice of neuro-oncology: A multidisciplinary approach. New York: Demos Medical; 2011 .p. 213.

Alotaibi NM, Noormohamed N, Cote DJ, Alharthi S, Doucette J, Zaidi HA, et al. Physiologic growth hormone-replacement therapy and craniopharyngioma recurrence in pediatric patients: A meta-analysis. World Neurosurg. 2017;09:165.

Unduhan

Diterbitkan

2024-03-01

Cara Mengutip

Christia, S., & Nurul Hidaya. (2024). Tata Laksana Kraniofaringioma Anak. Cermin Dunia Kedokteran, 51(3), 134–139. https://doi.org/10.55175/cdk.v51i3.904

Terbitan

Bagian

Articles